Endobronchial mucoepidermoid carcinoma in a child with postinfectious bronchiolitis obliterans

Data de publicação: Data Ahead of Print:

Autores da FMUP

  • Maria Inês Ferreira Agueda De Azevedo

    Autor

Participantes de fora da FMUP

  • Fonseca, S
  • Silva, S
  • Magalhaes, A
  • Lago, R
  • Estevinho, N
  • do Bom Sucesso, M

Unidades de investigação

Abstract

Endobronchial mucoepidermoid tumors are rare neoplasms. Due to nonspecific symptoms, diagnosis can be challenging, but early diagnosis and treatment are crucial for prognosis. We present the case of a boy, with chronic respiratory insufficiency due to bronchiolitis obliterans, that presented worsening exertional dyspnea at 12 years. Spirometry showed unexpected deterioration of respiratory function and a computed tomography scan revealed an obstructive polypoid mass in the intermediate bronchus. Given the severe basal ventilatory compromise and risk associated with surgical treatment, rigid bronchoscopy, and laser photocoagulation were performed, with clinical and functional improvement. The histological examination revealed a low-grade mucoepidermoid carcinoma. The option for a minimally invasive procedure requires careful follow-up due to the risk of tumor recurrence.

Dados da publicação

ISSN/ISSNe:
8755-6863, 1099-0496

Pediatric Pulmonology  Wiley-Liss Inc.

Tipo:
Article
Páginas:
4063-4065
Link para outro recurso:
www.scopus.com

Citações Recebidas na Web of Science: 2

Citações Recebidas na Scopus: 1

Documentos

  • Não há documentos

Métricas

Filiações mostrar / ocultar

Keywords

  • bronchoscopy; child; endobronchial mucoepidermoid carcinoma; laser; photocoagulation

Proyectos asociados

Hospitalizations for Varicella in children and adolescents in Portugal: 2000 to 2015

Investigador Principal: Maria Inês Ferreira Agueda de Azevedo

Estudo Clínico Académico (Varicella) . 2020

Pulmonary Auscultation using Mobile Devices - Feasibility Study in Respiratory Diseases

Investigador Principal: Maria Inês Ferreira Agueda de Azevedo

Estudo Clínico Académico . 2021

Citar a publicação

Partilhar a publicação